Improvement of Niemann Pick (B) Disease: Report of a Case Treated with Iranian Traditional Medicine

Document Type: Case reports or series

Authors

1 Traditional Medicine Clinical Trial Research Center, Shahed University, Tehran, Iran.

2 Department of Pediatric Gastroenterology, Ali-Asghar Children’s Hospital, School of Medicine, Iran University of Medical Sciences (I.U.M.S), Tehran, Iran.

Abstract

Background: Niemann-Pick Disease (NPD) is a rare autosomal recessive disorder associated with intracellular deposition of sphingomyelin and cholesterol storage within the lysosome. There are mainly three types of NPD namely types A, B, and C. NPD type B is generally later in onset with a good prognosis for survival into adulthood and usually with no neurological abnormalities.
Case Presentation: The patient, male, was born in 35 weeks of pregnancy. Failure to thrive started at around 4 months and the diagnosis of type B Niemann-Pick disease was made approximately at the age of 2 years. Currently, the patient is 10 years old and having undergone 3 years of Traditional Persian Diet, has had obvious improvement in growth and laboratory tests.
Conclusion: The NPD is no specific treatment, especially in modern medicine. Considering the significant improvement in the patient’s condition after an appropriate diet and traditional medicines, it seems that traditional medicinal therapies have great results in the treatment of NPD. In this study, we presented an innovation for NPD treatment by the use of a Traditional Persian diet.

Graphical Abstract

Improvement of Niemann Pick (B) Disease: Report of a Case Treated with Iranian Traditional Medicine

Keywords


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